A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve

A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve

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Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interv...

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Main Authors: Georges Khoueiry, Tariq Bhat, Mohmad Tantray, Mustafain Meghani, Nidal Abi Rafeh, Mokhtar Abdallah, Wissam Hoyek
Format: Article
Language:English
Published: SAGE Publishing 2014-01-01
Series:Clinical Medicine Insights: Circulatory, Respiratory and Pulmonary Medicine
Online Access:https://doi.org/10.4137/CCRPM.S11174
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spelling doaj-17cbdd381edc4ad3b834c3dd5c41f7722020-11-25T03:32:43ZengSAGE PublishingClinical Medicine Insights: Circulatory, Respiratory and Pulmonary Medicine1179-54842014-01-01810.4137/CCRPM.S11174A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary ValveGeorges Khoueiry0Tariq Bhat1Mohmad Tantray2Mustafain Meghani3Nidal Abi Rafeh4Mokhtar Abdallah5Wissam Hoyek6Department of Cardiology, Staten Island University Hospital, Staten Island, NY.Department of Cardiology, Staten Island University Hospital, Staten Island, NY.Department of Medicine, Staten Island University Hospital, Staten Island, NY.Department of Medicine, Staten Island University Hospital, Staten Island, NY.Department of Cardiology, Staten Island University Hospital, Staten Island, NY.Department of Medicine, Staten Island University Hospital, Staten Island, NY.Department of Cardiology, Staten Island University Hospital, Staten Island, NY.Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interventricular septum to the RV free wall. We are reporting a case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve, a rare form of congenital infundibular pulmonary stenosis. In addition to ventricular septal defect, our patient had congenital absence of the pulmonary valve, which is very unusual and has never been reported to our knowledge.https://doi.org/10.4137/CCRPM.S11174
collection DOAJ
language English
format Article
sources DOAJ
author Georges Khoueiry
Tariq Bhat
Mohmad Tantray
Mustafain Meghani
Nidal Abi Rafeh
Mokhtar Abdallah
Wissam Hoyek
spellingShingle Georges Khoueiry
Tariq Bhat
Mohmad Tantray
Mustafain Meghani
Nidal Abi Rafeh
Mokhtar Abdallah
Wissam Hoyek
A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve
Clinical Medicine Insights: Circulatory, Respiratory and Pulmonary Medicine
author_facet Georges Khoueiry
Tariq Bhat
Mohmad Tantray
Mustafain Meghani
Nidal Abi Rafeh
Mokhtar Abdallah
Wissam Hoyek
author_sort Georges Khoueiry
title A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve
title_short A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve
title_full A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve
title_fullStr A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve
title_full_unstemmed A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve
title_sort rare case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve
publisher SAGE Publishing
series Clinical Medicine Insights: Circulatory, Respiratory and Pulmonary Medicine
issn 1179-5484
publishDate 2014-01-01
description Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interventricular septum to the RV free wall. We are reporting a case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve, a rare form of congenital infundibular pulmonary stenosis. In addition to ventricular septal defect, our patient had congenital absence of the pulmonary valve, which is very unusual and has never been reported to our knowledge.
url https://doi.org/10.4137/CCRPM.S11174
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