El Síndrome del Hombre rígido o Síndrome de la persona rígida. Presentación de un caso

• Main Authors: Miguel Angel Serra Valdes, Ernesto Milán Ginjaune, Marleny García Viera, Juan Carlos Laurencio Espinosa, Liudmila Carnesolta Suárez, Jorge Luis Valdés Fuster
• Format: Article
• Language: English
• Published: Universidad de Ciencias Médicas de La Habana 2014-10-01
• Series: Revista Habanera de Ciencias Médicas
• Online Access: http://www.revhabanera.sld.cu/index.php/rhab/article/view/482

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La Clínica, la Resonancia Magnética Nuclear (RMN), Electromiografía y otros estudios permitieron el diagnóstico. <strong style="mso-bidi-font-weight: normal;">Discusión: </strong>Los recursos terapéuticos son limitados y se señala son poco alentadores los resultados. Progresa y causa seria discapacidad hasta llegar a la invalidez. Los pacientes tienen una pobre calidad de la vida, serias afectaciones psicológicas y económicas y un índice excesivo de comorbilidad y hospitalizaciones. <strong style="mso-bidi-font-weight: normal;">Conclusiones:</strong> Es una entidad infrecuente tanto para el clínico como el neurólogo. Es una patología de difícil diagnóstico.<span style="mso-spacerun: yes;"> </span>Es el primer reporte en más de 50 años de creado nuestro centro hospitalario. </span></p> <p class="MsoNormal" style="text-align: justify; line-height: 150%;"><strong style="mso-bidi-font-weight: normal;"><span style="font-family: &quot;Arial&quot;,&quot;sans-serif&quot;;">Palabras clave:</span></strong><span style="font-family: &quot;Arial&quot;,&quot;sans-serif&quot;;"> Síndrome de persona rígida, estado de invalidez, RMN, Electromiografía, adulto.</span></p> <!--[if gte mso 9]><xml> <w:LatentStyles DefLockedState="false" DefUnhideWhenUsed="true" DefSemiHidden="true" DefQFormat="false" DefPriority="99" LatentStyleCount="267"> <w:LsdException Locked="false" Priority="0" SemiHidden="false" UnhideWhenUsed="false" QFormat="true" Name="Normal" /> <w:LsdException Locked="false" Priority="9" SemiHidden="false" UnhideWhenUsed="false" QFormat="true" Name="heading 1" /> <w:LsdException Locked="false" Priority="9" 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