Glycosylation and the cystic fibrosis transmembrane conductance regulator

Glycosylation and the cystic fibrosis transmembrane conductance regulator

<p>Abstract</p> <p>The cystic fibrosis transmembrane conductance regulator (CFTR) has been known for the past 11 years to be a membrane glycoprotein with chloride channel activity. Only recently has the glycosylation of CFTR been examined in detail, by O'Riordan <it>et a...

Full description

Bibliographic Details
Main Authors:	Glick Mary Catherine, Scanlin Thomas F
Format:	Article
Language:	English
Published:	BMC 2001-08-01
Series:	Respiratory Research
Subjects:	ΔF508 cystic fibrosis transmembrane conductance regulator (CFTR) oligosaccharides polylactosamine
Online Access:	http://respiratory-research.com/content/2/5/276

Similar Items

Unravelling the Regions of Mutant F508del-CFTR More Susceptible to the Action of Four Cystic Fibrosis Correctors
by: Giulia Amico, et al.
Published: (2019-11-01)

Phenotype and Genotype of Two Taiwanese Cystic Fibrosis Siblings and a Survey of Delta F508 in East Asians
by: Chao-Jen Lin, et al.
Published: (2008-12-01)

Respiratory Syncytial Virus Infection Disrupts Monolayer Integrity and Function in Cystic Fibrosis Airway Cells
by: Wayne Sullender, et al.
Published: (2013-09-01)

p.F508del in a heterogeneous cystic fibrosis population from Minas Gerais, Brazil
by: P.V.T. Vidigal, et al.
Published: (2008-08-01)

State of the Art on Approved Cystic Fibrosis Transmembrane Conductance Regulator (<i>CFTR</i>) Modulators and Triple-Combination Therapy
by: Aniello Meoli, et al.
Published: (2021-09-01)

Common CFTR gene mutations in cystic fibrosis patients in Mazandaran province - Iran
by: Haleh Akhavan-Niaki (PhD), et al.
Published: (2008-10-01)

Activity of lumacaftor is not conserved in zebrafish Cftr bearing the major cystic fibrosis‐causing mutation
by: Onofrio Laselva, et al.
Published: (2019-10-01)

Impact de la modulation de TRPM7 et ATF6 sur le cystic fibrosis transmembrane conductance regulator
by: Huguet, Florentin
Published: (2017)

XV-2c and KM: 19 haplotype analysis in Chilean patients with cystic fibrosis and unknown CFTR gene mutations
by: GABRIELA M REPETTO, et al.
Published: (2007-01-01)

Genetic modification of cystic fibrosis with ΔF508 mutation of CFTR gene using the CRISPR system in peripheral blood mononuclear cells
by: Sepideh Khatibi, et al.
Published: (2021-01-01)

Ferret CFTR processing and function
by: Fisher, John T.
Published: (2012)

Frequency of 8 CFTR gene mutations in cystic fibrosis patients in Minas Gerais, Brazil, diagnosed by neonatal screening
by: C. Perone, et al.
Published: (2010-02-01)

'CFTR-opathies': disease phenotypes associated with cystic fibrosis transmembrane regulator gene mutations
by: Knowles Michael R, et al.
Published: (2001-08-01)

Frequency of the deltaF508 mutation in 108 cystic fibrosis patients in São Paulo: comparison with reported Brazilian data Freqüência da mutação deltaF508 em 108 pacientes com fibrose cística de São Paulo: comparação com dados de estudos brasileiros
by: Thelma Suely Okay, et al.
Published: (2005-04-01)

R117H mutation of the gene encoding the cystic fibrosis transmembrane regulatory protein in patients with chronic relapsing pancreatitis
by: Rodica BUGAI, et al.
Published: (2019-12-01)

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Ubiquitylation as a Novel Pharmaceutical Target for Cystic Fibrosis
by: Ryosuke Fukuda, et al.
Published: (2020-04-01)

Evaluation of Fused Pyrrolothiazole Systems as Correctors of Mutant CFTR Protein
by: Virginia Spanò, et al.
Published: (2021-02-01)

Fibrosis Quística Pulmonar, Gástrica y Gastro-Pulmonar en la Actualidad: Una Revisión Sistémica
by: C Bocanegra Amaya, et al.
Published: (2015-01-01)

CFTR Modulators: Impact on Fertility, Pregnancy, and Lactation in Women with Cystic Fibrosis
by: Jennifer L. Taylor-Cousar
Published: (2020-08-01)

Cystic Fibrosis: Overview of the Current Development Trends and Innovative Therapeutic Strategies
by: Fahad A. Almughem, et al.
Published: (2020-07-01)

Synthesis and Therapeutic Applications of Iminosugars in Cystic Fibrosis
by: Anna Esposito, et al.
Published: (2020-05-01)

Lentiviral Vectors and Cystic Fibrosis Gene Therapy
by: Massimo Conese, et al.
Published: (2010-01-01)

Prevalência da mutação ΔF508 no gene cystic fibrosis transmembrane conductance regulator em pacientes com fibrose cística em um centro de referência no Brasil
by: Andréia Marisa Bieger, et al.
Published: (2012-12-01)

Role of ATP binding and hydrolysis in the gating of the cystic fibrosis transmembrane conductance regulator
by: Taras Gout
Published: (2012-01-01)

Two years of newborn screening for cystic fibrosis in North Macedonia: First experience
by: Fustik S, et al.
Published: (2021-07-01)

Emerging microRNA Therapeutic Approaches for Cystic Fibrosis
by: Pauline Bardin, et al.
Published: (2018-10-01)

The Role of the Di-arginine "R553AR555" Motif in Modulating Trafficking and Function of the Major Cystic Fibrosis Causing Mutant (DeltaF508-CFTR)
by: Kim Chiaw, Patrick
Published: (2010)

The Role of the Di-arginine "R553AR555" Motif in Modulating Trafficking and Function of the Major Cystic Fibrosis Causing Mutant (DeltaF508-CFTR)
by: Kim Chiaw, Patrick
Published: (2010)

The role of cystic fibrosis transmembrane conductance regulator (CFTR) in ovarian functions.
Published: (2012)

Expression and functional significance of the cystic fibrosis transmembrane conductance regulator (CFTR) in human mast cells
by: Dry, Ren
Published: (2009)

Molecular analysis of CFTR gene mutations among Iraqi cystic fibrosis patients
by: Asal Gailan Abdul-Qadir, et al.
Published: (2021-05-01)

The Expression and Characterization of Human Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) in Tobacco
by: Witt, William T.
Published: (2014)

Structure and function of the cystic fibrosis transmembrane conductance regulator
by: M.M. Morales, et al.
Published: (1999-08-01)

Real-World Outcomes of Ivacaftor Treatment in People with Cystic Fibrosis: A Systematic Review
by: Jamie Duckers, et al.
Published: (2021-04-01)

Approaching two decades of cystic fibrosis research in Qatar: a historical perspective and future directions
by: Samer Hammoudeh, et al.
Published: (2019-10-01)

Comparative analyses of long non-coding RNA profiles in vivo in cystic fibrosis lung airway and parenchyma tissues
by: Parameet Kumar, et al.
Published: (2019-12-01)

Two Siblings Homozygous for F508del-CFTR Have Varied Disease Phenotypes and Protein Biomarkers
by: Zhihong Zhang, et al.
Published: (2021-03-01)

Regulation of a COX-2/PGE₂ by cystic fibrosis transmembrane conductance regulator: implications in inflammation and infertility.
Published: (2012)

A Novel Cystic Fibrosis Gene Mutation C.4242+1G>C in an Omani Patient: A Case Report
by: Said Al Balushi, et al.
Published: (2021-03-01)

Cystic fibrosis transmembrane conductance regulator modulators in cystic fibrosis: current perspectives
by: Schmidt BZ, et al.
Published: (2016-09-01)