Ruptured visceral artery aneurysms in a patient of neurofibromatosis type 1 (NF-1) successfully treated by endovascular treatment

• Main Authors: Naoko Fukushima, Hiroaki Aoki, Shinsuke Takenaga, Kazuhiko Morikawa, Masaichi Ogawa, Katsuhiko Yanaga
• Format: Article
• Language: English
• Published: SpringerOpen 2020-01-01
• Series: Surgical Case Reports
• Subjects: Visceral artery aneurysms; Neurofibromatosis type 1; Endovascular treatment
• Online Access: https://doi.org/10.1186/s40792-020-0791-6

Abstract Background Neurofibromatosis type 1 (NF-1) is an autosomal dominant disease and arteriovenous abnormalities are a well-recognized complication. There are several case reports of ruptured aneurysms; however, among them, reports of superior pancreaticoduodenal artery (PDA) and superior mesenteric artery (SMA) aneurysms are rare. We experienced the case of ruptured PDA and SMA aneurysms in a patient of neurofibromatosis type I successfully treated by endovascular treatment. Case presentation A 55-year-old woman with NF-1 came to our hospital with abdominal pain and vomiting. Enhanced abdominal computed tomography revealed a hematoma in the retroperitoneum and an aneurysm in the head of the pancreas. Angiography was performed, and a ruptured aneurysm was suspected the periphery of the PDA, and we embolized it using coils. However, on postoperative day 2, the hemoglobin level decreased, and a branch of the SMA was ruptured. She underwent embolization using coils again and discharged on postoperative day 27 without any further hemorrhage. Conclusions To our knowledge, this is the first successfully treated case of ruptured SMA and PDA aneurysms in a patient with NF-1.