A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt

A 19-year-old male patient presented cyanosis and dyspnoea because of the presence of multiple pulmonary arteriovenous fistulas resulting in oxygen desaturation. The CTA revealed that intestinal and splenic venous blood bypasses the liver and drains into the inferior vena cava. This is the first rep...

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Main Authors: Xue-Yan Ding, Feng Chen, Xian-Xian Zhao, Hong Wu, Shao-Ping Chen, Yong-Wen Qin
Format: Article
Language:English
Published: Hindawi Limited 2011-01-01
Series:Case Reports in Vascular Medicine
Online Access:http://dx.doi.org/10.1155/2011/508171
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spelling doaj-0f8a130c27764ceea7bc75786a6d5b522020-11-24T23:14:28ZengHindawi LimitedCase Reports in Vascular Medicine2090-69862090-69942011-01-01201110.1155/2011/508171508171A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic ShuntXue-Yan Ding0Feng Chen1Xian-Xian Zhao2Hong Wu3Shao-Ping Chen4Yong-Wen Qin5Department of Cardiology, Changhai Hospital, Second Military Medical University, Shanghai 200433, ChinaDepartment of Cardiology, Changhai Hospital, Second Military Medical University, Shanghai 200433, ChinaDepartment of Cardiology, Changhai Hospital, Second Military Medical University, Shanghai 200433, ChinaDepartment of Cardiology, Changhai Hospital, Second Military Medical University, Shanghai 200433, ChinaDepartment of Cardiology, Changhai Hospital, Second Military Medical University, Shanghai 200433, ChinaDepartment of Cardiology, Changhai Hospital, Second Military Medical University, Shanghai 200433, ChinaA 19-year-old male patient presented cyanosis and dyspnoea because of the presence of multiple pulmonary arteriovenous fistulas resulting in oxygen desaturation. The CTA revealed that intestinal and splenic venous blood bypasses the liver and drains into the inferior vena cava. This is the first reported case of hepatopulmonary syndrome caused by congenital extrahepatic portosystemic shunt in which intestinal and splenic venous blood bypasses the liver and drains into the inferior vena cava.http://dx.doi.org/10.1155/2011/508171
collection DOAJ
language English
format Article
sources DOAJ
author Xue-Yan Ding
Feng Chen
Xian-Xian Zhao
Hong Wu
Shao-Ping Chen
Yong-Wen Qin
spellingShingle Xue-Yan Ding
Feng Chen
Xian-Xian Zhao
Hong Wu
Shao-Ping Chen
Yong-Wen Qin
A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt
Case Reports in Vascular Medicine
author_facet Xue-Yan Ding
Feng Chen
Xian-Xian Zhao
Hong Wu
Shao-Ping Chen
Yong-Wen Qin
author_sort Xue-Yan Ding
title A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt
title_short A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt
title_full A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt
title_fullStr A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt
title_full_unstemmed A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt
title_sort rare cause of cyanosis: hepatopulmonary syndrome caused by congenital extrahepatic portosystemic shunt
publisher Hindawi Limited
series Case Reports in Vascular Medicine
issn 2090-6986
2090-6994
publishDate 2011-01-01
description A 19-year-old male patient presented cyanosis and dyspnoea because of the presence of multiple pulmonary arteriovenous fistulas resulting in oxygen desaturation. The CTA revealed that intestinal and splenic venous blood bypasses the liver and drains into the inferior vena cava. This is the first reported case of hepatopulmonary syndrome caused by congenital extrahepatic portosystemic shunt in which intestinal and splenic venous blood bypasses the liver and drains into the inferior vena cava.
url http://dx.doi.org/10.1155/2011/508171
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