Lymphangioleiomyomatosis: a clinical review

Lymphangioleiomyomatosis (LAM) is a diffuse cystic lung disease. There are two main types of LAM: sporadic, and LAM associated with the tuberous sclerosis complex (TSC), which is caused by mutations in the TSC1 and TSC2 genes. LAM is characterised by cystic lung disease resulting in progressive dysp...

Full description

Bibliographic Details
Main Authors: Anne M. O'Mahony, Evelyn Lynn, David J. Murphy, Aurelie Fabre, Cormac McCarthy
Format: Article
Language:English
Published: European Respiratory Society 2020-06-01
Series:Breathe
Online Access:http://breathe.ersjournals.com/content/16/2/200007.full