Pulmonary alveolar proteinosis: from classification to therapy
Pulmonary alveolar proteinosis (PAP) is a rare respiratory syndrome characterised by the accumulation of surfactant lipoproteins within the alveoli. According to various pathogenetic mechanisms and aetiologies, PAP is classified as primary, secondary or congenital. Primary PAP is led by a granulocyt...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
| Published: |
European Respiratory Society
2020-06-01
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| Series: | Breathe |
| Online Access: | http://breathe.ersjournals.com/content/16/2/200018.full |