Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue

Erdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presen...

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Main Authors: Jonghyun Byeon, Kyung Ah Kim, Seong Su Hwang, Soo Youn Park, Hyun A Kim
Format: Article
Language:English
Published: The Korean Society of Radiology 2015-02-01
Series:대한영상의학회지
Subjects:
Online Access:https://doi.org/10.3348/jksr.2015.72.2.143
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spelling doaj-082327502f91471eaf875db138dc327b2020-11-25T02:04:51ZengThe Korean Society of Radiology대한영상의학회지1738-26372288-29282015-02-01722143146https://doi.org/10.3348/jksr.2015.72.2.143Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat TissueJonghyun ByeonKyung Ah KimSeong Su HwangSoo Youn ParkHyun A KimErdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presented with bilateral perirenal masses containing fat tissue. He was diagnosed as perirenal involvement of Erdheim-Chester disease. This report describes a case of Erdheim-Chester disease with perirenal involvement that demonstrates unusual features. https://doi.org/10.3348/jksr.2015.72.2.143erdheim-chester diseasenon-langerhans-cell histiocytosiskidneyretroperitoneal fibrosis
collection DOAJ
language English
format Article
sources DOAJ
author Jonghyun Byeon
Kyung Ah Kim
Seong Su Hwang
Soo Youn Park
Hyun A Kim
spellingShingle Jonghyun Byeon
Kyung Ah Kim
Seong Su Hwang
Soo Youn Park
Hyun A Kim
Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
대한영상의학회지
erdheim-chester disease
non-langerhans-cell histiocytosis
kidney
retroperitoneal fibrosis
author_facet Jonghyun Byeon
Kyung Ah Kim
Seong Su Hwang
Soo Youn Park
Hyun A Kim
author_sort Jonghyun Byeon
title Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
title_short Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
title_full Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
title_fullStr Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
title_full_unstemmed Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
title_sort erdheim-chester disease with perirenal masses containing macroscopic fat tissue
publisher The Korean Society of Radiology
series 대한영상의학회지
issn 1738-2637
2288-2928
publishDate 2015-02-01
description Erdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presented with bilateral perirenal masses containing fat tissue. He was diagnosed as perirenal involvement of Erdheim-Chester disease. This report describes a case of Erdheim-Chester disease with perirenal involvement that demonstrates unusual features.
topic erdheim-chester disease
non-langerhans-cell histiocytosis
kidney
retroperitoneal fibrosis
url https://doi.org/10.3348/jksr.2015.72.2.143
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AT kyungahkim erdheimchesterdiseasewithperirenalmassescontainingmacroscopicfattissue
AT seongsuhwang erdheimchesterdiseasewithperirenalmassescontainingmacroscopicfattissue
AT sooyounpark erdheimchesterdiseasewithperirenalmassescontainingmacroscopicfattissue
AT hyunakim erdheimchesterdiseasewithperirenalmassescontainingmacroscopicfattissue
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