Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report

Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma...

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Main Authors: Yang Il Park, Ji Young Yoo, Joon Seog Kong
Format: Article
Language:English
Published: The Korean Society of Radiology 2021-09-01
Series:대한영상의학회지
Subjects:
Online Access:https://doi.org/10.3348/jksr.2020.0206
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spelling doaj-073529b48311477eac9d8bed88bbcb852021-09-30T05:26:52ZengThe Korean Society of Radiology대한영상의학회지2288-29282021-09-0182513461351https://doi.org/10.3348/jksr.2020.0206Osteosarcomatous Transformation in Mazabraud Syndrome: A Case ReportYang Il ParkJi Young YooJoon Seog KongMazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma, in Mazabraud syndrome have been reported worldwide. The authors report the first case of osteosarcomatous transformation in a patient with Mazabraud syndrome in the Republic of Korea, focusing on imaging findings.https://doi.org/10.3348/jksr.2020.0206mazabraud syndrometransformationneoplastic cellfibrous dysplasia of bonemyxoma; osteosarcomamagnetic resonance
collection DOAJ
language English
format Article
sources DOAJ
author Yang Il Park
Ji Young Yoo
Joon Seog Kong
spellingShingle Yang Il Park
Ji Young Yoo
Joon Seog Kong
Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
대한영상의학회지
mazabraud syndrome
transformation
neoplastic cell
fibrous dysplasia of bone
myxoma; osteosarcoma
magnetic resonance
author_facet Yang Il Park
Ji Young Yoo
Joon Seog Kong
author_sort Yang Il Park
title Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
title_short Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
title_full Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
title_fullStr Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
title_full_unstemmed Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
title_sort osteosarcomatous transformation in mazabraud syndrome: a case report
publisher The Korean Society of Radiology
series 대한영상의학회지
issn 2288-2928
publishDate 2021-09-01
description Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma, in Mazabraud syndrome have been reported worldwide. The authors report the first case of osteosarcomatous transformation in a patient with Mazabraud syndrome in the Republic of Korea, focusing on imaging findings.
topic mazabraud syndrome
transformation
neoplastic cell
fibrous dysplasia of bone
myxoma; osteosarcoma
magnetic resonance
url https://doi.org/10.3348/jksr.2020.0206
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AT jiyoungyoo osteosarcomatoustransformationinmazabraudsyndromeacasereport
AT joonseogkong osteosarcomatoustransformationinmazabraudsyndromeacasereport
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