Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report

Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report

Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma...

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Bibliographic Details
Main Authors: Yang Il Park, Ji Young Yoo, Joon Seog Kong
Format: Article
Language:English
Published: The Korean Society of Radiology 2021-09-01
Series:대한영상의학회지
Subjects:
mazabraud syndrome
transformation
neoplastic cell
fibrous dysplasia of bone
myxoma; osteosarcoma
magnetic resonance
Online Access:https://doi.org/10.3348/jksr.2020.0206
Description
Summary:Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma, in Mazabraud syndrome have been reported worldwide. The authors report the first case of osteosarcomatous transformation in a patient with Mazabraud syndrome in the Republic of Korea, focusing on imaging findings.
ISSN:2288-2928

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