Branch retinal artery occlusion in Susac's syndrome

• Main Authors: Ricardo Evangelista Marrocos de Aragão, Lorena Maria Araújo Gomes, Ieda Maria Alexandre Barreira, Francisco Holanda Oliveira Neto, Ariane Sá Vieira Bastos
• Format: Article
• Language: English
• Published: Sociedade Brasileira de Oftalmologia 2015-02-01
• Series: Revista Brasileira de Oftalmologia
• Subjects: Vasculite; Transtornos cerebrovasculares; Oclusão da artéria retiniana; Perda auditiva; Síndrome de Susac
• Online Access: http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0034-72802015000100040&lng=en&tlng=en

Susac's syndrome is a rare disease attribuited to a microangiopathy involving the arterioles of the cochlea, retina and brain. Encefalopathy, hearing loss, and visual deficits are the hallmarks of the disease. Visual loss is due to multiple, recurrent branch arterial retinal occlusions. We report a case of a 20-year-old women with Susac syndrome presented with peripheral vestibular syndrome, hearing loss, ataxia, vertigo, and vision loss due occlusion of the retinal branch artery.