Angiome plan de la face: À propos de deux cas dont l’un révélant un syndrome de Sturge Weber et Krabb

• Main Authors: Bénilde Marie Ange Tiemtoré-Kambou, Nomtondo Amina Ouédraogo, Nina-Astrid Ndé/Ouédraogo, Fagnima Traoré, Pakisba Ali Ouédraogo, Ben Aziz Dao, Boubacar Ouattara, Moussa Zanga, Ousséini Diallo, Rabiou Cissé
• Format: Article
• Language: English
• Published: Our Dermatology Online 2017-01-01
• Series: Nasza Dermatologia Online
• Subjects: Sturge weber syndrome; Glaucoma; Epilepsy
• Online Access: http://www.odermatol.com/issue-in-html/2017-1-19-angioma/

Sturge Weber and Krabbe syndrome or Sturge weber Syndrome (SWS) is a rare and sporadic disease. It associates with a variety of degrees a flat facial skin angioma in the V1 territory of the trigeminal, a pial angioma and a choroidal angioma all in the one side. The neurological involvement of epileptic seizures in fact all the gravity. The authors report two cases of angiomas plane of the face. The first case presents a complete association of the 3 signs in a 5 year old child. The second case presents an association of angioma and choroidal involvement without cerebral damage to imaging in a 25-year-old adult. They thus highlight the interest of imaging examinations in particular MRI in the diagnosis through the classification and follow-up of this pathology.