Rescue of murine F508del CFTR activity in native intestine by low temperature and proteasome inhibitors.

by Martina Wilke, Alice Bot, Huub Jorna, Bob J Scholte, Hugo R de Jonge
Published 2012-01-01

No indications for altered essential fatty acid metabolism in two murine models for cystic fibrosis

by Anniek Werner, Marloes E.J. Bongers, Marcel J. Bijvelds, Hugo R. de Jonge, Henkjan J. Verkade
Published 2004-12-01

Molecular Basis and Differentiation-Associated Alterations of Anion Secretion in Human Duodenal Enteroid MonolayersSummary

by Jianyi Yin, Chung-Ming Tse, Leela Rani Avula, Varsha Singh, Jennifer Foulke-Abel, Hugo R. de Jonge, Mark Donowitz
Published 2018-01-01

Assessing cell-specific effects of genetic variations using tRNA microarrays

by Christine Polte, Daniel Wedemeyer, Kathryn E. Oliver, Johannes Wagner, Marcel J. C. Bijvelds, John Mahoney, Hugo R. de Jonge, Eric J. Sorscher, Zoya Ignatova
Published 2019-07-01

Cholic acid induces a Cftr dependent biliary secretion and liver growth response in mice.

by Frank A J A Bodewes, Marcel J Bijvelds, Willemien de Vries, Juul F W Baller, Annette S H Gouw, Hugo R de Jonge, Henkjan J Verkade
Published 2015-01-01

Impaired Intestinal Farnesoid X Receptor Signaling in Cystic Fibrosis MiceSummary

by Pauline T. Ikpa, Marcela Doktorova, Kelly F. Meijsen, Natascha D.A. Nieuwenhuijze, Henkjan J. Verkade, Johan W. Jonker, Hugo R. de Jonge, Marcel J.C. Bijvelds
Published 2020-01-01

Biopolymer Extracted from <i>Anadenanthera colubrina</i> (Red Angico Gum) Exerts Therapeutic Potential in Mice: Antidiarrheal Activity and Safety Assessment

by Thiago S. L. Araújo, Taiane M. de Oliveira, Nayara A. de Sousa, Luan K.M. Souza, Francisca B. M. Sousa, Ana P. de Oliveira, Lucas A. D. Nicolau, Alfredo A. V. da Silva, Alyne R. Araújo, Pedro J. C. Magalhães, Daniel F. P. Vasconcelos, Hugo R. de Jonge, Marcellus H. L. P. Souza, Durcilene A. Silva, Regina C. M. Paula, Jand Venes R. Medeiros
Published 2020-01-01

Human extrahepatic and intrahepatic cholangiocyte organoids show region-specific differentiation potential and model cystic fibrosis-related bile duct disease

by Monique M. A. Verstegen, Floris J. M. Roos, Ksenia Burka, Helmuth Gehart, Myrthe Jager, Maaike de Wolf, Marcel J. C. Bijvelds, Hugo R. de Jonge, Arif I. Ardisasmita, Nick A. van Huizen, Henk P. Roest, Jeroen de Jonge, Michael Koch, Francesco Pampaloni, Sabine A. Fuchs, Imre F. Schene, Theo M. Luider, Hubert P. J. van der Doef, Frank A. J. A. Bodewes, Ruben H. J. de Kleine, Bart Spee, Gert-Jan Kremers, Hans Clevers, Jan N. M. IJzermans, Edwin Cuppen, Luc J. W. van der Laan
Published 2020-12-01

Rectal Organoids Enable Personalized Treatment of Cystic Fibrosis

by Gitte Berkers, Peter van Mourik, Annelotte M. Vonk, Evelien Kruisselbrink, Johanna F. Dekkers, Karin M. de Winter-de Groot, Hubertus G.M. Arets, Rozemarijn E.P. Marck-van der Wilt, Jasper S. Dijkema, Maaike M. Vanderschuren, Roderick H.J. Houwen, Harry G.M. Heijerman, Eduard A. van de Graaf, Sjoerd G. Elias, Christof J. Majoor, Gerard H. Koppelman, Jolt Roukema, Marleen Bakker, Hettie M. Janssens, Renske van der Meer, Robert G.J. Vries, Hans C. Clevers, Hugo R. de Jonge, Jeffrey M. Beekman, Cornelis K. van der Ent
Published 2019-02-01